Summary

Aggressive angiomyxoma is a mesenchymal tumor that is frequently found in women of reproductive age mostly appearing in the vulva, perineal region, head, neck, trunk, and lower limbs. A 33-year-old multiparous Somali woman presented to the outpatient department of Dr Sumait Hospital, with a complaint of swelling around her vulva. The patient reported that the mass had progressively grown for the past 8 years and that she experienced stigma from her previous spouses. Her past medical history and socioeconomic status were unremarkable. During the physical examination, a well-defined pedunculated mass measuring 14 cm × 8 cm, originating from the labia majora, was noted. The mass was pinkish, non-tender, non-reducible, and had a soft consistency. Some areas of ulceration measuring 2 cm × 2 cm, covered with necrotic granulation tissues, were also noticed. With the patient’s written informed consent, a biopsy was performed, and the histopathology results revealed aggressive angiomyxoma. Following confirmation of the diagnosis, the mass was surgically excised under sterile conditions and spinal anesthesia. Aggressive angiomyxoma is an important consideration when evaluating vulvovaginal growth in females. Given its tendency for local recurrences, it is vital to establish an accurate diagnosis.